Glycine, serine and threonine metabolism |    |
Glutathione metabolism |    |
beta-Alanine metabolism |    |
Lysine degradation |    |
Sulfur metabolism |    |
Purine metabolism |    |
Tyrosine metabolism |    |
Tryptophan metabolism |    |
Valine, leucine and isoleucine degradation |    |
Nicotinate and nicotinamide metabolism |    |
Arginine and proline metabolism |    |
Phenylalanine and Tyrosine Metabolism |    |
Vitamin B6 Metabolism |    |
Porphyrin Metabolism |    |
Caffeine Metabolism |    |
Methionine Metabolism |    |
D-Arginine and D-Ornithine Metabolism |    |
Histidine metabolism |    |
Aspartate Metabolism |    |
Riboflavin Metabolism |    |
Arachidonic Acid Metabolism |    |
Ibuprofen Action Pathway |    |
2-Methyl-3-Hydroxybutryl CoA Dehydrogenase Deficiency |    |
3-Hydroxy-3-Methylglutaryl-CoA Lyase Deficiency |    |
3-Methylglutaconic Aciduria Type I |    |
3-Methylglutaconic Aciduria Type III |    |
3-Methylglutaconic Aciduria Type IV |    |
5-Oxoprolinuria |    |
Adenosine Deaminase Deficiency |    |
Adenylosuccinate Lyase Deficiency |    |
AICA-Ribosiduria |    |
Alkaptonuria |    |
Beta-Ketothiolase Deficiency |    |
Canavan Disease |    |
Cystathionine Beta-Synthase Deficiency |    |
Dihydropyrimidine Dehydrogenase Deficiency (DHPD) |    |
Gamma-Glutamyltransferase Deficiency |    |
Glutaric Aciduria Type I |    |
Guanidinoacetate Methyltransferase Deficiency (GAMT Deficiency) |    |
Hawkinsinuria |    |
Histidinemia |    |
Hypoacetylaspartia |    |
Maple Syrup Urine Disease |    |
Methylmalonic Aciduria |    |
Molybdenum Cofactor Deficiency |    |
Phenylketonuria |    |
Prolidase Deficiency (PD) |    |
Prolinemia Type II |    |
Purine Nucleoside Phosphorylase Deficiency |    |
S-Adenosylhomocysteine (SAH) Hydrolase Deficiency |    |
Tyrosinemia Type I |    |
Xanthine Dehydrogenase Deficiency (Xanthinuria) |    |
Methionine Adenosyltransferase Deficiency |    |
Glycine N-methyltransferase Deficiency |    |
Non Ketotic Hyperglycinemia |    |
Propionic Acidemia |    |
3-Methylcrotonyl Coa Carboxylase Deficiency Type I |    |
Isovaleric Aciduria |    |
Saccharopinuria/Hyperlysinemia II |    |
Dimethylglycine Dehydrogenase Deficiency |    |
Sarcosinemia |    |
Clopidogrel Action Pathway |    |
Glutathione Synthetase Deficiency |    |
Methylenetetrahydrofolate Reductase Deficiency (MTHFRD) |    |
Hypermethioninemia |    |
Hereditary Coproporphyria (HCP) |    |
Acute Intermittent Porphyria |    |
Congenital Erythropoietic Porphyria (CEP) or Gunther Disease |    |
Porphyria Variegata (PV) |    |
GABA-Transaminase Deficiency |    |
Hyperprolinemia Type II |    |
Hyperprolinemia Type I |    |
Arginine: Glycine Amidinotransferase Deficiency (AGAT Deficiency) |    |
Ornithine Aminotransferase Deficiency (OAT Deficiency) |    |
Lesch-Nyhan Syndrome (LNS) |    |
Gout or Kelley-Seegmiller Syndrome |    |
Tyrosinemia Type 2 (or Richner-Hanhart syndrome) |    |
Tyrosinemia Type 3 (TYRO3) |    |
Methylmalonate Semialdehyde Dehydrogenase Deficiency |    |
Citalopram Action Pathway |    |
Azathioprine Action Pathway |    |
Mercaptopurine Action Pathway |    |
Disulfiram Action Pathway |    |
Thioguanine Action Pathway |    |
Nicotine Action Pathway |    |
Cyclophosphamide Action Pathway |    |
Ifosfamide Action Pathway |    |
Ethanol Degradation |    |
Degradation of Superoxides |    |
Plasmalogen Synthesis |    |
Dimethylglycine Dehydrogenase Deficiency |    |
Hyperglycinemia, non-ketotic |    |
Ureidopropionase Deficiency |    |
Carnosinuria, carnosinemia |    |
Tyrosinemia, transient, of the newborn |    |
Dopamine beta-hydroxylase deficiency |    |
5-oxoprolinase deficiency |    |
Gamma-glutamyl-transpeptidase deficiency |    |
Hypophosphatasia |    |
Creatine deficiency, guanidinoacetate methyltransferase deficiency |    |
Hyperornithinemia with gyrate atrophy (HOGA) |    |
Hyperornithinemia-hyperammonemia-homocitrullinuria [HHH-syndrome] |    |
L-arginine:glycine amidinotransferase deficiency |    |
Xanthinuria type I |    |
Xanthinuria type II |    |
3-hydroxyisobutyric acid dehydrogenase deficiency |    |
3-hydroxyisobutyric aciduria |    |
Isobutyryl-coa dehydrogenase deficiency |    |
Isovaleric acidemia |    |
Hyperlysinemia I, Familial |    |
Hyperlysinemia II or Saccharopinuria |    |
Sulfite oxidase deficiency |    |
Monoamine oxidase-a deficiency (MAO-A) |    |
Adenine phosphoribosyltransferase deficiency (APRT) |    |
Mitochondrial DNA depletion syndrome |    |
Myoadenylate deaminase deficiency |    |
Homocystinuria-megaloblastic anemia due to defect in cobalamin metabolism, cblG complementation type |    |
Pyridoxine dependency with seizures |    |
Ibuprofen Metabolism Pathway |    |
Cyclophosphamide Metabolism Pathway |    |
Ifosfamide Metabolism Pathway |    |
Clopidogrel Metabolism Pathway |    |
Citalopram Metabolism Pathway |    |
Nicotine Metabolism Pathway |    |
Nevirapine Metabolism Pathway |    |
Sorafenib Metabolism Pathway |    |
Lamivudine Metabolism Pathway |    |
Thyroid hormone synthesis |    |
2-aminoadipic 2-oxoadipic aciduria |    |
3-Phosphoglycerate dehydrogenase deficiency |    |