Arginine and proline metabolism |    |
beta-Alanine metabolism |    |
Nitrogen metabolism |    |
Purine metabolism |    |
Tyrosine metabolism |    |
Citrullinemia Type I |    |
Carbamoyl Phosphate Synthetase Deficiency |    |
Argininosuccinic Aciduria |    |
Transcription/Translation |    |
Urea Cycle |    |
Aspartate Metabolism |    |
Glutamate Metabolism |    |
Malate-Aspartate Shuttle |    |
2-Hydroxyglutric Aciduria (D And L Form) |    |
Adenosine Deaminase Deficiency |    |
Adenylosuccinate Lyase Deficiency |    |
AICA-Ribosiduria |    |
Alkaptonuria |    |
Canavan Disease |    |
Guanidinoacetate Methyltransferase Deficiency (GAMT Deficiency) |    |
Hawkinsinuria |    |
Hypoacetylaspartia |    |
Molybdenum Cofactor Deficiency |    |
Ornithine Transcarbamylase Deficiency (OTC Deficiency) |    |
Prolidase Deficiency (PD) |    |
Prolinemia Type II |    |
Purine Nucleoside Phosphorylase Deficiency |    |
Tyrosinemia Type I |    |
Xanthine Dehydrogenase Deficiency (Xanthinuria) |    |
4-Hydroxybutyric Aciduria/Succinic Semialdehyde Dehydrogenase Deficiency |    |
Hyperinsulinism-Hyperammonemia Syndrome |    |
GABA-Transaminase Deficiency |    |
Argininemia |    |
Hyperprolinemia Type II |    |
Hyperprolinemia Type I |    |
Arginine: Glycine Amidinotransferase Deficiency (AGAT Deficiency) |    |
Ornithine Aminotransferase Deficiency (OAT Deficiency) |    |
Lesch-Nyhan Syndrome (LNS) |    |
Gout or Kelley-Seegmiller Syndrome |    |
Homocarnosinosis |    |
Azathioprine Action Pathway |    |
Mercaptopurine Action Pathway |    |
Disulfiram Action Pathway |    |
Thioguanine Action Pathway |    |
Ureidopropionase Deficiency |    |
Carnosinuria, carnosinemia |    |
Tyrosinemia, transient, of the newborn |    |
Dopamine beta-hydroxylase deficiency |    |
Creatine deficiency, guanidinoacetate methyltransferase deficiency |    |
Hyperornithinemia with gyrate atrophy (HOGA) |    |
Hyperornithinemia-hyperammonemia-homocitrullinuria [HHH-syndrome] |    |
L-arginine:glycine amidinotransferase deficiency |    |
Xanthinuria type I |    |
Xanthinuria type II |    |
Monoamine oxidase-a deficiency (MAO-A) |    |
Adenine phosphoribosyltransferase deficiency (APRT) |    |
Mitochondrial DNA depletion syndrome |    |
Myoadenylate deaminase deficiency |    |
Succinic semialdehyde dehydrogenase deficiency |    |
Glutaminolysis and Cancer |    |