Valine, leucine and isoleucine degradation |    |
Propanoate metabolism |    |
Lysine degradation |    |
Pyruvate metabolism |    |
beta-Alanine metabolism |    |
Biosynthesis of unsaturated fatty acids |    |
Glycine, serine and threonine metabolism |    |
Tryptophan metabolism |    |
Steroid Biosynthesis |    |
Caffeine Metabolism |    |
Oxidation of Branched Chain Fatty Acids |    |
Amino Sugar Metabolism |    |
Fatty acid Metabolism |    |
Fatty Acid Elongation In Mitochondria |    |
Citric Acid Cycle |    |
Ketone Body Metabolism |    |
Glutamate Metabolism |    |
Butyrate Metabolism |    |
Retinol Metabolism |    |
Ibandronate Action Pathway |    |
Simvastatin Action Pathway |    |
Pravastatin Action Pathway |    |
Rosuvastatin Action Pathway |    |
Alendronate Action Pathway |    |
Lovastatin Action Pathway |    |
Zoledronate Action Pathway |    |
Cerivastatin Action Pathway |    |
Risedronate Action Pathway |    |
Pamidronate Action Pathway |    |
Fluvastatin Action Pathway |    |
Atorvastatin Action Pathway |    |
2-Hydroxyglutric Aciduria (D And L Form) |    |
2-Methyl-3-Hydroxybutryl CoA Dehydrogenase Deficiency |    |
3-Hydroxy-3-Methylglutaryl-CoA Lyase Deficiency |    |
3-Methylglutaconic Aciduria Type I |    |
3-Methylglutaconic Aciduria Type III |    |
3-Methylglutaconic Aciduria Type IV |    |
Beta-Ketothiolase Deficiency |    |
Dihydropyrimidine Dehydrogenase Deficiency (DHPD) |    |
Ethylmalonic Encephalopathy |    |
Glutaric Aciduria Type I |    |
Glutaric Aciduria Type I |    |
Leigh Syndrome |    |
Malonic Aciduria |    |
Maple Syrup Urine Disease |    |
Methylmalonic Aciduria |    |
Methylmalonic Aciduria Due to Cobalamin-Related Disorders |    |
Hypercholesterolemia |    |
Pyruvate Dehydrogenase Complex Deficiency |    |
Sialuria or French Type Sialuria |    |
Non Ketotic Hyperglycinemia |    |
Short Chain Acyl CoA Dehydrogenase Deficiency (SCAD Deficiency) |    |
Propionic Acidemia |    |
3-Methylcrotonyl Coa Carboxylase Deficiency Type I |    |
Isovaleric Aciduria |    |
Saccharopinuria/Hyperlysinemia II |    |
Salla Disease/Infantile Sialic Acid Storage Disease |    |
Dimethylglycine Dehydrogenase Deficiency |    |
4-Hydroxybutyric Aciduria/Succinic Semialdehyde Dehydrogenase Deficiency |    |
Sarcosinemia |    |
Lysosomal Acid Lipase Deficiency (Wolman Disease) |    |
Pyruvate Decarboxylase E1 Component Deficiency (PDHE1 Deficiency) |    |
Vitamin A Deficiency |    |
Hyperinsulinism-Hyperammonemia Syndrome |    |
GABA-Transaminase Deficiency |    |
Methylmalonate Semialdehyde Dehydrogenase Deficiency |    |
Homocarnosinosis |    |
Desmosterolosis |    |
CHILD Syndrome |    |
Chondrodysplasia Punctata II, X Linked Dominant (CDPX2) |    |
Smith-Lemli-Opitz Syndrome (SLOS) |    |
Tay-Sachs Disease |    |
Disulfiram Action Pathway |    |
Ethanol Degradation |    |
Phytanic Acid Peroxisomal Oxidation |    |
Refsum Disease |    |
Fatty Acid Biosynthesis |    |
Transfer of Acetyl Groups into Mitochondria |    |
Mitochondrial Beta-Oxidation of Short Chain Saturated Fatty Acids |    |
Mitochondrial Beta-Oxidation of Medium Chain Saturated Fatty Acids |    |
Mitochondrial Beta-Oxidation of Long Chain Saturated Fatty Acids |    |
Dimethylglycine Dehydrogenase Deficiency |    |
Hyperglycinemia, non-ketotic |    |
Ureidopropionase Deficiency |    |
Carnosinuria, carnosinemia |    |
Malonyl-coa decarboxylase deficiency |    |
Cholesteryl ester storage disease |    |
Hyper-IgD syndrome |    |
Mevalonic aciduria |    |
Wolman disease |    |
Adrenoleukodystrophy, X-linked |    |
Carnitine-acylcarnitine translocase deficiency |    |
3-hydroxyisobutyric acid dehydrogenase deficiency |    |
3-hydroxyisobutyric aciduria |    |
Isobutyryl-coa dehydrogenase deficiency |    |
Isovaleric acidemia |    |
Hyperlysinemia I, Familial |    |
Hyperlysinemia II or Saccharopinuria |    |
G(M2)-Gangliosidosis: Variant B, Tay-sachs disease |    |
Carnitine palmitoyl transferase deficiency (I) |    |
Long chain acyl-CoA dehydrogenase deficiency (LCAD) |    |
Very-long-chain acyl coa dehydrogenase deficiency (VLCAD) |    |
Carnitine palmitoyl transferase deficiency (II) |    |
Medium chain acyl-coa dehydrogenase deficiency (MCAD) |    |
Long-chain-3-hydroxyacyl-coa dehydrogenase deficiency (LCHAD) |    |
Trifunctional protein deficiency |    |
Congenital lactic acidosis |    |
Fumarase deficiency |    |
Mitochondrial complex II deficiency |    |
2-ketoglutarate dehydrogenase complex deficiency |    |
Pyruvate dehydrogenase deficiency (E3) |    |
Pyruvate dehydrogenase deficiency (E2) |    |
Primary hyperoxaluria II, PH2 |    |
Pyruvate kinase deficiency |    |
Succinic semialdehyde dehydrogenase deficiency |    |
Short-chain 3-hydroxyacyl-CoA dehydrogenase deficiency (SCHAD) |    |
Succinyl CoA: 3-ketoacid CoA transferase deficiency |    |
Pyridoxine dependency with seizures |    |
Warburg Effect |    |
2-aminoadipic 2-oxoadipic aciduria |    |
3-Phosphoglycerate dehydrogenase deficiency |    |
Acylcarnitine 3-Hydroxydecanoylcarnitine |    |
Acylcarnitine (7Z,9Z,12Z,15Z,18Z,21Z)-tetracosa-7,9,12,15,18,21-hexaenoylcarnitine |    |
Acylcarnitine Pentacosanoylcarnitine |    |
Acylcarnitine Hexacosanoylcarnitine |    |
Acylcarnitine (17Z)-Hexacos-17-enoylcarnitine |    |
Acylcarnitine (13Z,16Z)-Hexacosa-13,16-dienoylcarnitine |    |
Acylcarnitine Heptacosanoylcarnitine |    |
Acylcarnitine Octacosanoylcarnitine |    |
Acylcarnitine Nonacosanoylcarnitine |    |
Acylcarnitine (2S,3R)-3-Hydroxy-2-methylbutanoylcarnitine |    |
The oncogenic action of 2-hydroxyglutarate |    |
The Oncogenic Action of Succinate |    |
The Oncogenic Action of Fumarate |    |
Glutaminolysis and Cancer |    |
The oncogenic action of L-2-hydroxyglutarate in Hydroxygluaricaciduria |    |
The oncogenic action of D-2-hydroxyglutarate in Hydroxygluaricaciduria |    |