Glutathione metabolism |    |
Arginine and proline metabolism |    |
beta-Alanine metabolism |    |
One carbon pool by folate |    |
Lysine degradation |    |
Valine, leucine and isoleucine degradation |    |
Pyruvate metabolism |    |
Purine metabolism |    |
Tyrosine metabolism |    |
Glycine, serine and threonine metabolism |    |
Pyrimidine metabolism |    |
Primary bile acid biosynthesis |    |
Tryptophan metabolism |    |
Oxidative phosphorylation |    |
Nicotinate and nicotinamide metabolism |    |
Propanoate metabolism |    |
Glycine, serine and threonine metabolism |    |
Nitrogen metabolism |    |
Phenylalanine and Tyrosine Metabolism |    |
Vitamin B6 Metabolism |    |
Steroid Biosynthesis |    |
Porphyrin Metabolism |    |
Phospholipid Biosynthesis |    |
Caffeine Metabolism |    |
Methionine Metabolism |    |
D-Arginine and D-Ornithine Metabolism |    |
Glycerolipid Metabolism |    |
Histidine metabolism |    |
Fatty acid Metabolism |    |
Citric Acid Cycle |    |
Aspartate Metabolism |    |
Riboflavin Metabolism |    |
Glutamate Metabolism |    |
Butyrate Metabolism |    |
Ibandronate Action Pathway |    |
Simvastatin Action Pathway |    |
Pravastatin Action Pathway |    |
Rosuvastatin Action Pathway |    |
Alendronate Action Pathway |    |
Lovastatin Action Pathway |    |
Zoledronate Action Pathway |    |
Cerivastatin Action Pathway |    |
Risedronate Action Pathway |    |
Pamidronate Action Pathway |    |
Fluvastatin Action Pathway |    |
Glycerol Phosphate Shuttle |    |
Atorvastatin Action Pathway |    |
2-Hydroxyglutric Aciduria (D And L Form) |    |
2-Methyl-3-Hydroxybutryl CoA Dehydrogenase Deficiency |    |
3-Hydroxy-3-Methylglutaryl-CoA Lyase Deficiency |    |
3-Methylglutaconic Aciduria Type I |    |
3-Methylglutaconic Aciduria Type III |    |
3-Methylglutaconic Aciduria Type IV |    |
5-Oxoprolinuria |    |
Adenosine Deaminase Deficiency |    |
Adenylosuccinate Lyase Deficiency |    |
AICA-Ribosiduria |    |
Alkaptonuria |    |
Beta Ureidopropionase Deficiency |    |
Beta-Ketothiolase Deficiency |    |
Canavan Disease |    |
Cystathionine Beta-Synthase Deficiency |    |
Dihydropyrimidinase Deficiency |    |
Dihydropyrimidine Dehydrogenase Deficiency (DHPD) |    |
Ethylmalonic Encephalopathy |    |
Gamma-Glutamyltransferase Deficiency |    |
Glutaric Aciduria Type I |    |
Glutaric Aciduria Type I |    |
Glycerol Kinase Deficiency |    |
Guanidinoacetate Methyltransferase Deficiency (GAMT Deficiency) |    |
Hawkinsinuria |    |
Histidinemia |    |
Hypoacetylaspartia |    |
Leigh Syndrome |    |
Malonic Aciduria |    |
Maple Syrup Urine Disease |    |
Methylmalonic Aciduria |    |
Methylmalonic Aciduria Due to Cobalamin-Related Disorders |    |
MNGIE (Mitochondrial Neurogastrointestinal Encephalopathy) |    |
Molybdenum Cofactor Deficiency |    |
Phenylketonuria |    |
Prolidase Deficiency (PD) |    |
Prolinemia Type II |    |
Hypercholesterolemia |    |
Purine Nucleoside Phosphorylase Deficiency |    |
Pyruvate Dehydrogenase Complex Deficiency |    |
S-Adenosylhomocysteine (SAH) Hydrolase Deficiency |    |
Tyrosinemia Type I |    |
UMP Synthase Deficiency (Orotic Aciduria) |    |
Xanthine Dehydrogenase Deficiency (Xanthinuria) |    |
Methionine Adenosyltransferase Deficiency |    |
Glycine N-methyltransferase Deficiency |    |
Non Ketotic Hyperglycinemia |    |
Short Chain Acyl CoA Dehydrogenase Deficiency (SCAD Deficiency) |    |
Propionic Acidemia |    |
3-Methylcrotonyl Coa Carboxylase Deficiency Type I |    |
Isovaleric Aciduria |    |
Saccharopinuria/Hyperlysinemia II |    |
Dimethylglycine Dehydrogenase Deficiency |    |
4-Hydroxybutyric Aciduria/Succinic Semialdehyde Dehydrogenase Deficiency |    |
Sarcosinemia |    |
Congenital Bile Acid Synthesis Defect Type II |    |
Cerebrotendinous Xanthomatosis (CTX) |    |
Zellweger Syndrome |    |
Familial Hypercholanemia (FHCA) |    |
Congenital Bile Acid Synthesis Defect Type III |    |
Lysosomal Acid Lipase Deficiency (Wolman Disease) |    |
Phenytoin (Antiarrhythmic) Action Pathway |    |
Pyruvate Decarboxylase E1 Component Deficiency (PDHE1 Deficiency) |    |
Glutathione Synthetase Deficiency |    |
Hyperinsulinism-Hyperammonemia Syndrome |    |
Methylenetetrahydrofolate Reductase Deficiency (MTHFRD) |    |
Hypermethioninemia |    |
Hereditary Coproporphyria (HCP) |    |
Acute Intermittent Porphyria |    |
Congenital Erythropoietic Porphyria (CEP) or Gunther Disease |    |
Porphyria Variegata (PV) |    |
GABA-Transaminase Deficiency |    |
Hyperprolinemia Type II |    |
Hyperprolinemia Type I |    |
Arginine: Glycine Amidinotransferase Deficiency (AGAT Deficiency) |    |
Ornithine Aminotransferase Deficiency (OAT Deficiency) |    |
Lesch-Nyhan Syndrome (LNS) |    |
Gout or Kelley-Seegmiller Syndrome |    |
Tyrosinemia Type 2 (or Richner-Hanhart syndrome) |    |
Tyrosinemia Type 3 (TYRO3) |    |
Methylmalonate Semialdehyde Dehydrogenase Deficiency |    |
Homocarnosinosis |    |
Desmosterolosis |    |
CHILD Syndrome |    |
Chondrodysplasia Punctata II, X Linked Dominant (CDPX2) |    |
Smith-Lemli-Opitz Syndrome (SLOS) |    |
Citalopram Action Pathway |    |
Azathioprine Action Pathway |    |
Mercaptopurine Action Pathway |    |
Disulfiram Action Pathway |    |
Thioguanine Action Pathway |    |
Nicotine Action Pathway |    |
Methotrexate Action Pathway |    |
Threonine and 2-Oxobutanoate Degradation |    |
Pyruvaldehyde Degradation |    |
Vitamin K Metabolism |    |
Capecitabine Action Pathway |    |
Tamoxifen Action Pathway |    |
Plasmalogen Synthesis |    |
Mitochondrial Beta-Oxidation of Short Chain Saturated Fatty Acids |    |
Mitochondrial Beta-Oxidation of Medium Chain Saturated Fatty Acids |    |
Mitochondrial Beta-Oxidation of Long Chain Saturated Fatty Acids |    |
Dimethylglycine Dehydrogenase Deficiency |    |
Hyperglycinemia, non-ketotic |    |
Ureidopropionase Deficiency |    |
Carnosinuria, carnosinemia |    |
Tyrosinemia, transient, of the newborn |    |
Dopamine beta-hydroxylase deficiency |    |
5-oxoprolinase deficiency |    |
Gamma-glutamyl-transpeptidase deficiency |    |
Malonyl-coa decarboxylase deficiency |    |
Hypophosphatasia |    |
Creatine deficiency, guanidinoacetate methyltransferase deficiency |    |
Hyperornithinemia with gyrate atrophy (HOGA) |    |
Hyperornithinemia-hyperammonemia-homocitrullinuria [HHH-syndrome] |    |
L-arginine:glycine amidinotransferase deficiency |    |
Cholesteryl ester storage disease |    |
Hyper-IgD syndrome |    |
Mevalonic aciduria |    |
Wolman disease |    |
Xanthinuria type I |    |
Xanthinuria type II |    |
3-hydroxyisobutyric acid dehydrogenase deficiency |    |
3-hydroxyisobutyric aciduria |    |
Isobutyryl-coa dehydrogenase deficiency |    |
Isovaleric acidemia |    |
Hyperlysinemia I, Familial |    |
Hyperlysinemia II or Saccharopinuria |    |
D-glyceric acidura |    |
Familial lipoprotein lipase deficiency |    |
Monoamine oxidase-a deficiency (MAO-A) |    |
Adenine phosphoribosyltransferase deficiency (APRT) |    |
Mitochondrial DNA depletion syndrome |    |
Myoadenylate deaminase deficiency |    |
Carnitine palmitoyl transferase deficiency (I) |    |
Long chain acyl-CoA dehydrogenase deficiency (LCAD) |    |
Very-long-chain acyl coa dehydrogenase deficiency (VLCAD) |    |
Carnitine palmitoyl transferase deficiency (II) |    |
Medium chain acyl-coa dehydrogenase deficiency (MCAD) |    |
Methylenetetrahydrofolate Reductase Deficiency (MTHFRD) |    |
Trifunctional protein deficiency |    |
Congenital lactic acidosis |    |
Fumarase deficiency |    |
Mitochondrial complex II deficiency |    |
2-ketoglutarate dehydrogenase complex deficiency |    |
Pyruvate dehydrogenase deficiency (E3) |    |
Pyruvate dehydrogenase deficiency (E2) |    |
Primary hyperoxaluria II, PH2 |    |
Pyruvate kinase deficiency |    |
Succinic semialdehyde dehydrogenase deficiency |    |
Short-chain 3-hydroxyacyl-CoA dehydrogenase deficiency (SCHAD) |    |
Homocystinuria-megaloblastic anemia due to defect in cobalamin metabolism, cblG complementation type |    |
Pyridoxine dependency with seizures |    |
Tamoxifen Metabolism Pathway |    |
Capecitabine Metabolism Pathway |    |
Mercaptopurine Metabolism Pathway |    |
Citalopram Metabolism Pathway |    |
Nicotine Metabolism Pathway |    |
Valproic Acid Metabolism Pathway |    |
Doxorubicin Metabolism Pathway |    |
Warburg Effect |    |
Thyroid hormone synthesis |    |
2-aminoadipic 2-oxoadipic aciduria |    |
27-Hydroxylase Deficiency |    |
3-Phosphoglycerate dehydrogenase deficiency |    |
Folate malabsorption, hereditary |    |
The oncogenic action of 2-hydroxyglutarate |    |
The Oncogenic Action of Succinate |    |
The Oncogenic Action of Fumarate |    |
Glutaminolysis and Cancer |    |
Sarcosine Oncometabolite Pathway |    |
The oncogenic action of L-2-hydroxyglutarate in Hydroxygluaricaciduria |    |
The oncogenic action of D-2-hydroxyglutarate in Hydroxygluaricaciduria |    |